Left Ventricular Non-Compaction Treatment
For children with left ventricular non-compaction cardiomyopathy (LVNC), treatment is focused on heart failure and reducing the risk of sudden cardiac death.
The treatment goals are to:
- Control symptoms of congestive heart failure
- Control ventricular arrhythmias
- Prevent sudden cardiac death
Common medications include:
- ACE inhibitors
- Beta-blockers to alleviate symptoms and potentially help the heart muscle structure to normalize.
- Anti-arrhythmic medications such as amiodarone or sotalol to prevent sudden death
- Anti-coagulants such as aspirin to prevent clot formation
- Mitochondrial metabolic disorder cocktail of Q10, thiamine, riboflavin, and carnitine for those with a metabolic disorder
For more advanced disease, other interventions may be necessary such as:
- Implantable pacemaker or defibrillator
- Mechanical ventilator support (intubation)
- Cardiac assist devices (ECMO, LVAD, BIVAD)
- Heart transplantation
To learn more about these treatment options, read the sections on Medication, Implantable Devices, Mechanical Cardiac Assist Devices, and Heart Transplantation.