Left Ventricular Non-Compaction Treatment

For children with left ventricular non-compaction cardiomyopathy (LVNC), treatment is focused on heart failure and reducing the risk of sudden cardiac death.

The treatment goals are to:

  • Control symptoms of congestive heart failure
  • Control ventricular arrhythmias
  • Prevent sudden cardiac death

Common medications include:

  • Diuretics
  • ACE inhibitors
  • Beta-blockers to alleviate symptoms and potentially help the heart muscle structure to normalize.
  • Anti-arrhythmic medications such as amiodarone or sotalol to prevent sudden death
  • Anti-coagulants such as aspirin to prevent clot formation
  • Mitochondrial metabolic disorder cocktail of Q10, thiamine, riboflavin, and carnitine for those with a metabolic disorder

For more advanced disease, other interventions may be necessary such as:

  • Implantable pacemaker or defibrillator
  • Mechanical ventilator support (intubation)
  • Cardiac assist devices (ECMO, LVAD, BIVAD)
  • Heart transplantation

To learn more about these treatment options, read the sections on Medication, Implantable DevicesMechanical Cardiac Assist Devices, and Heart Transplantation.

Medication

 

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